C83.0 vs C88.0
C83.0 and C88.0 can never be reported together. ICD-10-CM declares them mutually exclusive with an Excludes1 note, meaning the two conditions cannot occur in the same patient — so exactly one of them is correct for any given encounter.
The official note, declared on C88.0
small cell B-cell lymphoma (C83.0)
C83.0
Small cell B-cell lymphoma
Not billable
- Chapter 2
- Neoplasms
- Section
- C81-C96
Use when the record says
- Lymphoplasmacytic lymphoma
- Nodal marginal zone lymphoma
- Non-leukemic variant of B-CLL
- Splenic marginal zone lymphoma
Indexed under
- Immunocytoma
- Lymphoma › lymphoplasmacytic (of) (malignant)
- Lymphoma › nodal marginal zone (of) (malignant)
- Lymphoma › non-leukemic variant of B-CLL (of) (malignant)
- Lymphoma › small cell B-cell (of) (malignant)
C88.0
Waldenstrom macroglobulinemia
Not billable
- Chapter 2
- Neoplasms
- Section
- C81-C96
Use when the record says
- Lymphoplasmacytic lymphoma with IgM-production
- Macroglobulinemia (idiopathic) (primary)
Indexed under
- Macroglobulinemia (idiopathic) (primary)
- Macroglobulinemia › Waldenström (idiopathic) (primary)
- Waldenström › syndrome or macroglobulinemia
- Disorder › glomerular › Waldenström macroglobulinemia (of)
- Glomerulonephritis › in › Waldenström macroglobulinemia
Excludes1 is not always absolute: where two conditions covered by the note are genuinely unrelated, CMS guidance permits reporting both. Document the reasoning rather than assuming it. More on Excludes1 vs Excludes2 · FY2027