Excludes1 pair

C00- vs C4A.0

C00 and C4A.0 are not coded together. ICD-10-CM declares them mutually exclusive with an Excludes1 note — the two conditions are not expected to occur together, so exactly one of them is normally correct for a given encounter. The Official Guidelines carve out one exception: if the two conditions are clearly unrelated to each other, both may be reported.

The official note, declared on C00
Merkel cell carcinoma of lip (C4A.0)
C00

Malignant neoplasm of lip

Not billable
Chapter 2
Neoplasms
Section
C00-C14
C4A.0

Merkel cell carcinoma of lip

Billable
Chapter 2
Neoplasms
Section
C43-C44
Indexed under
  • Carcinoma › Merkel cell › lip

Excludes1 is not always absolute: where two conditions covered by the note are genuinely unrelated, CMS guidance permits reporting both. Document the reasoning rather than assuming it. More on Excludes1 vs Excludes2 · FY2027