Excludes1 pair

C00.2 vs C4A.0

C00.2 and C4A.0 are not coded together. ICD-10-CM declares them mutually exclusive with an Excludes1 note — the two conditions are not expected to occur together, so exactly one of them is normally correct for a given encounter. The Official Guidelines carve out one exception: if the two conditions are clearly unrelated to each other, both may be reported.

The official note, declared on C4A.0
malignant neoplasm of vermilion border of lip (C00.0-C00.2)
C00.2

Malignant neoplasm of external lip, unspecified

BillableUnspecified
Chapter 2
Neoplasms
Section
C00-C14
Use when the record says
  • Malignant neoplasm of vermilion border of lip NOS
C4A.0

Merkel cell carcinoma of lip

Billable
Chapter 2
Neoplasms
Section
C43-C44
Indexed under
  • Carcinoma › Merkel cell › lip

Excludes1 is not always absolute: where two conditions covered by the note are genuinely unrelated, CMS guidance permits reporting both. Document the reasoning rather than assuming it. More on Excludes1 vs Excludes2 · FY2027