ICDcodes.org
FY2027

Q85.89Other phakomatoses, not elsewhere classified

BillableUnspecifiedCC

Is Q85.89 billable?

Yes, but Q85.89 is an unspecified code. Q85.89 is a valid, billable ICD-10-CM code for encounters from October 1, 2026 through September 30, 2027. However, Q85.89 is an unspecified or catch-all code. Payers apply additional scrutiny to unspecified codes and many deny them when the medical record supports a more specific option, so check the documentation before selecting Q85.89 — the more specific alternatives are listed below.

Q85.89 at a glance

CodeQ85.89
DescriptionOther phakomatoses, not elsewhere classified
BillableYes
Code setICD-10-CM FY2027
Valid for encountersOctober 1, 2026 – September 30, 2027

Which MS-DRGs does Q85.89 group to?

Q85.89 sits in MDC 17 and helps define the logic of 3 MS-DRGs (version 44, FY2027). Which one a stay actually groups to also depends on procedures and secondary diagnoses.

  • 826Myeloproliferative Disorders or Poorly Differentiated Neoplasms with Major O.R. Procedures with MCCsurgical
  • 827Myeloproliferative Disorders or Poorly Differentiated Neoplasms with Major O.R. Procedures with CCsurgical
  • 828Myeloproliferative Disorders or Poorly Differentiated Neoplasms with Major O.R. Procedures without CC/MCCsurgical

As a secondary diagnosis, Q85.89 is a complication or comorbidity (CC), which can move a stay into a higher-paying DRG.

How is Q85.89 listed in the Alphabetic Index?

These are the routes through the Alphabetic Index that lead to Q85.89. They show the wording a clinician may have documented, which often differs from the Tabular description.

  • Dimitri-Sturge-Weber disease
  • Kraft-Weber-Dimitri disease
  • Peutz-Jeghers disease or syndrome
  • Sturgedisease or syndrome (-Weber) (-Dimitri) (-Kalischer)
  • Angiomatosisencephalotrigeminal
  • Phakomatosisspecified NEC
  • SyndromePeutz-Jeghers
  • SyndromeSturge-Weber

Inclusion terms

Alternative wording in documentation that is classified to Q85.89.

  • Peutz-Jeghers syndrome
  • Sturge-Weber(-Dimitri) syndrome

Excludes1 — never code together — inherited from Q85

The conditions below can never be reported together with Q85.89 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.

  • ataxia telangiectasia [Louis-Bar] (G11.3)
  • familial dysautonomia [Riley-Day] (G90.1)

Excludes1 — never code together — inherited from Q85.8

The conditions below can never be reported together with Q85.89 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.

  • Meckel-Gruber syndrome (Q61.9)

Excludes2 — not included here — inherited from Chapter 17

The conditions below are not part of Q85.89, but a patient may have both at the same time. When documentation supports it, Q85.89 and the excluded code may both be reported.

  • inborn errors of metabolism (E70-E88)

How long has Q85.89 existed?

Q85.89 first appears in FY2023.

Derived from the official order files for FY2016–FY2026. FY2017 and FY2020 publish no order file, so those years are not covered.

Which conditions are coded to Q85.89?

What other codes are in the Q85.8 family? (3)