Q43.1 — Hirschsprung's disease

BillableCC

Is Q43.1 billable?

Yes — Q43.1 is billable for FY2027. Q43.1 is a valid, billable ICD-10-CM code at the highest level of specificity in its branch. Q43.1 may be submitted for encounters from October 1, 2026 through September 30, 2027.

Q43.1 at a glance

Code	Q43.1
Description	Hirschsprung's disease
Billable	Yes
Code set	ICD-10-CM FY2027
Valid for encounters	October 1, 2026 – September 30, 2027

Which MS-DRGs does Q43.1 group to?

Q43.1 sits in MDC 06 and helps define the logic of 3 MS-DRGs (version 44, FY2027). Which one a stay actually groups to also depends on procedures and secondary diagnoses.

393Other Digestive System Diagnoses with MCCmedical
394Other Digestive System Diagnoses with CCmedical
395Other Digestive System Diagnoses without CC/MCCmedical

As a secondary diagnosis, Q43.1 is a complication or comorbidity (CC), which can move a stay into a higher-paying DRG.

How is Q43.1 listed in the Alphabetic Index?

These are the routes through the Alphabetic Index that lead to Q43.1. They show the wording a clinician may have documented, which often differs from the Tabular description.

Aganglionosis (bowel) (colon)
Hirschsprung's disease or megacolon
Macrocolon
Megacolon › congenital, congenitum (acquired) (functional) (not Hirschsprung's disease) (in)
Megacolon › Hirschsprung's (acquired) (functional) (not Hirschsprung's disease) (in)
Dilatation › colon › congenital
Ileus › neurogenic › Hirschsprung's disease or megacolon (bowel) (colon) (inhibitory) (intestine)
Obstruction, obstructed, obstructive › intestine › neurogenic › Hirschsprung's disease or megacolon

Inclusion terms

Alternative wording in documentation that is classified to Q43.1.

Aganglionosis
Congenital (aganglionic) megacolon

Excludes2 — not included here — inherited from Chapter 17

The conditions below are not part of Q43.1, but a patient may have both at the same time. When documentation supports it, Q43.1 and the excluded code may both be reported.

inborn errors of metabolism (E70-E88)

How long has Q43.1 existed?

Q43.1 has been in ICD-10-CM since at least FY2016, the earliest fiscal year on record here.

Derived from the official order files for FY2016–FY2026. FY2017 and FY2020 publish no order file, so those years are not covered.

Which codes are confused with Q43.1?

ICD-10-CM declares these codes mutually exclusive with Q43.1 — exactly one of each pair can be correct for a given encounter.