Q40.0 — Congenital hypertrophic pyloric stenosis
Is Q40.0 billable?
Yes — Q40.0 is billable for FY2027. Q40.0 is a valid, billable ICD-10-CM code at the highest level of specificity in its branch. Q40.0 may be submitted for encounters from October 1, 2026 through September 30, 2027.
Q40.0 at a glance
| Code | Q40.0 |
|---|---|
| Description | Congenital hypertrophic pyloric stenosis |
| Billable | Yes |
| Code set | ICD-10-CM FY2027 |
| Valid for encounters | October 1, 2026 – September 30, 2027 |
Which MS-DRGs does Q40.0 group to?
Q40.0 sits in MDC 06 and helps define the logic of 3 MS-DRGs (version 44, FY2027). Which one a stay actually groups to also depends on procedures and secondary diagnoses.
- 393Other Digestive System Diagnoses with MCCmedical
- 394Other Digestive System Diagnoses with CCmedical
- 395Other Digestive System Diagnoses without CC/MCCmedical
How is Q40.0 listed in the Alphabetic Index?
These are the routes through the Alphabetic Index that lead to Q40.0. They show the wording a clinician may have documented, which often differs from the Tabular description.
- Achalasia › pylorus (cardia) (esophagus)
- PylorospasmNEC › congenital (reflex)
- PylorospasmNEC › newborn (reflex)
- Constriction › pylorus › congenital
- Constriction › pylorus › newborn
- Hypertrophy, hypertrophic › pylorus › congenital
- Obstruction, obstructed, obstructive › pylorus › congenital
- Spasm, spastic, spasticity › pylorus NEC › congenital (s)
- Stenosis, stenotic › pylorus › congenital (cicatricial)
- Stricture › pylorus › congenital
Inclusion terms
Alternative wording in documentation that is classified to Q40.0.
- Congenital constriction
- Congenital hypertrophy
- Congenital spasm
- Congenital stenosis
- Congenital stricture
Excludes2 — not included here — inherited from Chapter 17
The conditions below are not part of Q40.0, but a patient may have both at the same time. When documentation supports it, Q40.0 and the excluded code may both be reported.
- inborn errors of metabolism (E70-E88)
How long has Q40.0 existed?
Q40.0 has been in ICD-10-CM since at least FY2016, the earliest fiscal year on record here.
Derived from the official order files for FY2016–FY2026. FY2017 and FY2020 publish no order file, so those years are not covered.
Which codes are confused with Q40.0?
ICD-10-CM declares these codes mutually exclusive with Q40.0 — exactly one of each pair can be correct for a given encounter.