ICDcodes.org
FY2027

H49.813Kearns-Sayre syndrome, bilateral

BillableCC

Is H49.813 billable?

Yes — H49.813 is billable for FY2027. H49.813 is a valid, billable ICD-10-CM code at the highest level of specificity in its branch. H49.813 may be submitted for encounters from October 1, 2026 through September 30, 2027.

H49.813 at a glance

CodeH49.813
DescriptionKearns-Sayre syndrome, bilateral
BillableYes
Code setICD-10-CM FY2027
Valid for encountersOctober 1, 2026 – September 30, 2027

Which MS-DRGs does H49.813 group to?

H49.813 sits in MDC 10 and helps define the logic of 1 MS-DRG (version 44, FY2027). Which one a stay actually groups to also depends on procedures and secondary diagnoses.

  • 642Inborn and Other Disorders of Metabolismmedical

As a secondary diagnosis, H49.813 is a complication or comorbidity (CC), which can move a stay into a higher-paying DRG.

How is H49.813 listed in the Alphabetic Index?

The Alphabetic Index lists these routes under H49.81, the nearest indexed parent of H49.813. Use them to find the family, then select the specific code.

  • Kearns-Sayre syndrome
  • StrabismusparalyticKearns-Sayre syndrome (congenital) (nonparalytic)
  • Strabismusparalyticophthalmoplegiaprogressivewith pigmentary retinopathy (congenital) (nonparalytic)

Excludes2 — not included here — inherited from Chapter 7

The conditions below are not part of H49.813, but a patient may have both at the same time. When documentation supports it, H49.813 and the excluded code may both be reported.

  • certain conditions originating in the perinatal period (P04-P96)
  • certain infectious and parasitic diseases (A00-B99)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
  • diabetes mellitus related eye conditions (E09.3-, E10.3-, E11.3-, E13.3-)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • injury (trauma) of eye and orbit (S05.-)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
  • syphilis related eye disorders (A50.01, A50.3-, A51.43, A52.71)

Excludes2 — not included here — inherited from H49-H52

The conditions below are not part of H49.813, but a patient may have both at the same time. When documentation supports it, H49.813 and the excluded code may both be reported.

  • nystagmus and other irregular eye movements (H55)

Excludes2 — not included here — inherited from H49

The conditions below are not part of H49.813, but a patient may have both at the same time. When documentation supports it, H49.813 and the excluded code may both be reported.

  • internal ophthalmoplegia (H52.51-)
  • internuclear ophthalmoplegia (H51.2-)
  • progressive supranuclear ophthalmoplegia (G23.1)

Code also — inherited from H49.81

Two codes may be needed to describe the condition fully. Whether H49.813 is sequenced first depends on the reason for the encounter.

  • , if applicable, other manifestations, such as:
  • heart block (I45.9)

How long has H49.813 existed?

H49.813 has been in ICD-10-CM since at least FY2016, the earliest fiscal year on record here.

Derived from the official order files for FY2016–FY2026. FY2017 and FY2020 publish no order file, so those years are not covered.

What other codes are in the H49.81 family? (3)