ICDcodes.org
FY2027

G40.42Cyclin-Dependent Kinase-Like 5 Deficiency Disorder

Billable

Is G40.42 billable?

Yes — G40.42 is billable for FY2027. G40.42 is a valid, billable ICD-10-CM code at the highest level of specificity in its branch. G40.42 may be submitted for encounters from October 1, 2026 through September 30, 2027.

G40.42 at a glance

CodeG40.42
DescriptionCyclin-Dependent Kinase-Like 5 Deficiency Disorder
BillableYes
Code setICD-10-CM FY2027
Valid for encountersOctober 1, 2026 – September 30, 2027

Which MS-DRGs does G40.42 group to?

G40.42 sits in MDC 01 and helps define the logic of 1 MS-DRG (version 44, FY2027). Which one a stay actually groups to also depends on procedures and secondary diagnoses.

  • 023Craniotomy with Major Device Implant or Acute Complex CNS Principal Diagnosis with MCC or Antineoplastic Implant or Epilepsy with Neurostimulatorsurgical

How is G40.42 listed in the Alphabetic Index?

These are the routes through the Alphabetic Index that lead to G40.42. They show the wording a clinician may have documented, which often differs from the Tabular description.

  • CDKL5 (Cyclin-Dependent Kinase-Like 5 Deficiency Disorder)
  • DisorderCyclin-Dependent Kinase-Like 5 Deficiency (of)

Use additional code

Report an additional code alongside G40.42 to fully describe the condition. G40.42 is sequenced first.

  • code, if known, to identify associated manifestations, such as:
  • cortical blindness (H47.61-)
  • global developmental delay (F88)

Inclusion terms

Alternative wording in documentation that is classified to G40.42.

  • CDKL5

Excludes1 — never code together — inherited from G40

The conditions below can never be reported together with G40.42 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.

  • conversion disorder with seizures (F44.5)
  • convulsions NOS (R56.9)
  • post traumatic seizures (R56.1)
  • seizure (convulsive) NOS (R56.9)
  • seizure of newborn (P90)

Excludes2 — not included here — inherited from Chapter 6

The conditions below are not part of G40.42, but a patient may have both at the same time. When documentation supports it, G40.42 and the excluded code may both be reported.

  • certain conditions originating in the perinatal period (P04-P96)
  • certain infectious and parasitic diseases (A00-B99)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)

Excludes2 — not included here — inherited from G40

The conditions below are not part of G40.42, but a patient may have both at the same time. When documentation supports it, G40.42 and the excluded code may both be reported.

How long has G40.42 existed?

G40.42 first appears in FY2021 (FY2020 is not available, so it may have appeared then).

Derived from the official order files for FY2016–FY2026. FY2017 and FY2020 publish no order file, so those years are not covered.

What other codes are in the G40.4 family? (2)