ICDcodes.org
FY2027

E76.219Morquio mucopolysaccharidoses, unspecified

BillableUnspecifiedCC

Is E76.219 billable?

Yes, but E76.219 is an unspecified code. E76.219 is a valid, billable ICD-10-CM code for encounters from October 1, 2026 through September 30, 2027. However, E76.219 is an unspecified or catch-all code. Payers apply additional scrutiny to unspecified codes and many deny them when the medical record supports a more specific option, so check the documentation before selecting E76.219 — the more specific alternatives are listed below.

E76.219 at a glance

CodeE76.219
DescriptionMorquio mucopolysaccharidoses, unspecified
BillableYes
Code setICD-10-CM FY2027
Valid for encountersOctober 1, 2026 – September 30, 2027

Which MS-DRGs does E76.219 group to?

E76.219 sits in MDC 10 and helps define the logic of 1 MS-DRG (version 44, FY2027). Which one a stay actually groups to also depends on procedures and secondary diagnoses.

  • 642Inborn and Other Disorders of Metabolismmedical

As a secondary diagnosis, E76.219 is a complication or comorbidity (CC), which can move a stay into a higher-paying DRG.

How is E76.219 listed in the Alphabetic Index?

These are the routes through the Alphabetic Index that lead to E76.219. They show the wording a clinician may have documented, which often differs from the Tabular description.

  • Chondro-osteodysplasia (Morquio-Brailsford type)
  • Kyphosis, kyphoticMorquio-Brailsford type (acquired)
  • MucopolysaccharidosisMorquio syndrome
  • MucopolysaccharidosistypeIV

Inclusion terms

Alternative wording in documentation that is classified to E76.219.

  • Morquio syndrome
  • Mucopolysaccharidosis, type IV

Excludes1 — never code together — inherited from Chapter 4

The conditions below can never be reported together with E76.219 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.

  • transitory endocrine and metabolic disorders specific to newborn (P70-P74)

Excludes1 — never code together — inherited from E70-E88

The conditions below can never be reported together with E76.219 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.

  • androgen insensitivity syndrome (E34.5-)
  • congenital adrenal hyperplasia (E25.0)
  • hemolytic anemias attributable to enzyme disorders (D55.-)
  • Marfan syndrome (Q87.4-)
  • 5-alpha-reductase deficiency (E29.1)

Excludes2 — not included here — inherited from E70-E88

The conditions below are not part of E76.219, but a patient may have both at the same time. When documentation supports it, E76.219 and the excluded code may both be reported.

  • Ehlers-Danlos syndromes (Q79.6-)

How long has E76.219 existed?

E76.219 has been in ICD-10-CM since at least FY2016, the earliest fiscal year on record here.

Derived from the official order files for FY2016–FY2026. FY2017 and FY2020 publish no order file, so those years are not covered.

Which conditions are coded to E76.219?

What other codes are in the E76.21 family? (2)