E71.541 — Zellweger-like syndrome
Is E71.541 billable?
Yes — E71.541 is billable for FY2027. E71.541 is a valid, billable ICD-10-CM code at the highest level of specificity in its branch. E71.541 may be submitted for encounters from October 1, 2026 through September 30, 2027.
E71.541 at a glance
| Code | E71.541 |
|---|---|
| Description | Zellweger-like syndrome |
| Billable | Yes |
| Code set | ICD-10-CM FY2027 |
| Valid for encounters | October 1, 2026 – September 30, 2027 |
Which MS-DRGs does E71.541 group to?
E71.541 sits in MDC 10 and helps define the logic of 1 MS-DRG (version 44, FY2027). Which one a stay actually groups to also depends on procedures and secondary diagnoses.
- 642Inborn and Other Disorders of Metabolismmedical
As a secondary diagnosis, E71.541 is a complication or comorbidity (CC), which can move a stay into a higher-paying DRG.
How is E71.541 listed in the Alphabetic Index?
These are the routes through the Alphabetic Index that lead to E71.541. They show the wording a clinician may have documented, which often differs from the Tabular description.
- Syndrome › Zellweger-like syndrome
- Disorder › peroxisomal › Zellweger-like syndrome (of)
Excludes1 — never code together — inherited from Chapter 4
The conditions below can never be reported together with E71.541 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.
- transitory endocrine and metabolic disorders specific to newborn (P70-P74)
Excludes1 — never code together — inherited from E70-E88
The conditions below can never be reported together with E71.541 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.
Excludes1 — never code together — inherited from E71.5
The conditions below can never be reported together with E71.541 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.
- Schilder's disease (G37.0)
Excludes2 — not included here — inherited from E70-E88
The conditions below are not part of E71.541, but a patient may have both at the same time. When documentation supports it, E71.541 and the excluded code may both be reported.
- Ehlers-Danlos syndromes (Q79.6-)
How long has E71.541 existed?
E71.541 has been in ICD-10-CM since at least FY2016, the earliest fiscal year on record here.
Derived from the official order files for FY2016–FY2026. FY2017 and FY2020 publish no order file, so those years are not covered.