ICDcodes.org
FY2027

E70.330Chediak-Higashi syndrome

BillableCC

Is E70.330 billable?

Yes — E70.330 is billable for FY2027. E70.330 is a valid, billable ICD-10-CM code at the highest level of specificity in its branch. E70.330 may be submitted for encounters from October 1, 2026 through September 30, 2027.

E70.330 at a glance

CodeE70.330
DescriptionChediak-Higashi syndrome
BillableYes
Code setICD-10-CM FY2027
Valid for encountersOctober 1, 2026 – September 30, 2027

Which MS-DRGs does E70.330 group to?

E70.330 sits in MDC 10 and helps define the logic of 1 MS-DRG (version 44, FY2027). Which one a stay actually groups to also depends on procedures and secondary diagnoses.

  • 642Inborn and Other Disorders of Metabolismmedical

As a secondary diagnosis, E70.330 is a complication or comorbidity (CC), which can move a stay into a higher-paying DRG.

How is E70.330 listed in the Alphabetic Index?

These are the routes through the Alphabetic Index that lead to E70.330. They show the wording a clinician may have documented, which often differs from the Tabular description.

  • Chédiak-Higashi (-Steinbrinck) syndrome (congenital gigantism of peroxidase granules)
  • Anomaly, anomalousChédiak-Higashi (congenital) (unspecified type)
  • Disease, diseasedChédiak-Steinbrinck
  • SyndromeBéquez César
  • SyndromeChédiak-Higashi
  • Albinism, albinowith hematologic abnormalityChédiak-Higashi syndrome

Excludes1 — never code together — inherited from Chapter 4

The conditions below can never be reported together with E70.330 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.

  • transitory endocrine and metabolic disorders specific to newborn (P70-P74)

Excludes1 — never code together — inherited from E70-E88

The conditions below can never be reported together with E70.330 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.

  • androgen insensitivity syndrome (E34.5-)
  • congenital adrenal hyperplasia (E25.0)
  • hemolytic anemias attributable to enzyme disorders (D55.-)
  • Marfan syndrome (Q87.4-)
  • 5-alpha-reductase deficiency (E29.1)

Excludes2 — not included here — inherited from E70-E88

The conditions below are not part of E70.330, but a patient may have both at the same time. When documentation supports it, E70.330 and the excluded code may both be reported.

  • Ehlers-Danlos syndromes (Q79.6-)

How long has E70.330 existed?

E70.330 has been in ICD-10-CM since at least FY2016, the earliest fiscal year on record here.

Derived from the official order files for FY2016–FY2026. FY2017 and FY2020 publish no order file, so those years are not covered.

Which conditions are coded to E70.330?

What other codes are in the E70.33 family? (3)