ICDcodes.org
FY2027

D81.39Other adenosine deaminase deficiency

BillableCC

Is D81.39 billable?

Yes — D81.39 is billable for FY2027. D81.39 is a valid, billable ICD-10-CM code at the highest level of specificity in its branch. D81.39 may be submitted for encounters from October 1, 2026 through September 30, 2027.

D81.39 at a glance

CodeD81.39
DescriptionOther adenosine deaminase deficiency
BillableYes
Code setICD-10-CM FY2027
Valid for encountersOctober 1, 2026 – September 30, 2027

Which MS-DRGs does D81.39 group to?

D81.39 sits in MDC 10 and helps define the logic of 1 MS-DRG (version 44, FY2027). Which one a stay actually groups to also depends on procedures and secondary diagnoses.

  • 642Inborn and Other Disorders of Metabolismmedical

As a secondary diagnosis, D81.39 is a complication or comorbidity (CC), which can move a stay into a higher-paying DRG.

How is D81.39 listed in the Alphabetic Index?

These are the routes through the Alphabetic Index that lead to D81.39. They show the wording a clinician may have documented, which often differs from the Tabular description.

  • Deficiency, deficientadenosine deaminasepartial
  • Deficiency, deficientadenosine deaminasespecified NEC
  • Deficiency, deficientadenosine deaminasetype 1

Inclusion terms

Alternative wording in documentation that is classified to D81.39.

  • Adenosine deaminase [ADA] deficiency type 1, NOS
  • Adenosine deaminase [ADA] deficiency type 1, without SCID
  • Adenosine deaminase [ADA] deficiency type 1, without severe combined immunodeficiency
  • Partial ADA deficiency (type 1)
  • Partial adenosine deaminase deficiency (type 1)

Excludes1 — never code together — inherited from D80-D89

The conditions below can never be reported together with D81.39 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.

  • autoimmune disease (systemic) NOS (M35.9)
  • functional disorders of polymorphonuclear neutrophils (D71-)

Excludes1 — never code together — inherited from D81

The conditions below can never be reported together with D81.39 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.

  • autosomal recessive agammaglobulinemia (Swiss type) (D80.0)

Excludes2 — not included here — inherited from Chapter 3

The conditions below are not part of D81.39, but a patient may have both at the same time. When documentation supports it, D81.39 and the excluded code may both be reported.

  • autoimmune disease (systemic) NOS (M35.9)
  • certain conditions originating in the perinatal period (P00-P96)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • human immunodeficiency virus [HIV] disease (B20)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)

Excludes2 — not included here — inherited from D80-D89

The conditions below are not part of D81.39, but a patient may have both at the same time. When documentation supports it, D81.39 and the excluded code may both be reported.

  • human immunodeficiency virus [HIV] disease (B20)

How long has D81.39 existed?

D81.39 first appears in FY2021 (FY2020 is not available, so it may have appeared then).

Derived from the official order files for FY2016–FY2026. FY2017 and FY2020 publish no order file, so those years are not covered.

What other codes are in the D81.3 family? (3)