ICD-10 Code for Ataxia
The ICD-10-CM code for ataxia is R27.0 — Ataxia, unspecified. This is the code the Alphabetic Index gives for ataxia with no further qualifier, valid for FY2027 (October 1, 2026 – September 30, 2027).
R27.0 is billable but unspecified. If the documentation names a type, site or cause, one of the more specific codes below is likely expected.
Which ataxia code should you use?
The Alphabetic Index lists 29 codes under Ataxia, ataxy, ataxic. Which one applies depends on the qualifier documented in the record — the type, site, cause, or associated condition. Find the qualifier below, then verify the code in the Tabular List before using it.
By type
| acute | R27.8 | Other lack of coordination | |
| autosomal recessive Friedreich | G11.11 | Friedreich ataxia | |
| brain | G11.9 | Hereditary ataxia, unspecified | |
| cerebellar | G11.9 | Hereditary ataxia, unspecified | |
| cerebral | G11.9 | Hereditary ataxia, unspecified | |
| congenital nonprogressive | G11.0 | Congenital nonprogressive ataxia | |
| Friedreich's | G11.11 | Friedreich ataxia | |
| gait | R26.0 | Ataxic gait | |
| general | R27.8 | Other lack of coordination | |
| gluten | M35.9 | Systemic involvement of connective tissue, unspecified | |
| hereditary | G11.9 | Hereditary ataxia, unspecified | |
| Hunt's | G11.19 | Other early-onset cerebellar ataxia | |
| hysterical | F44.4 | Conversion disorder with motor symptom or deficit | |
| locomotor | A52.11 | Tabes dorsalis | |
| Marie's | G11.2 | Late-onset cerebellar ataxia | |
| nonorganic origin | F44.4 | Conversion disorder with motor symptom or deficit | |
| nonprogressive, congenital | G11.0 | Congenital nonprogressive ataxia | |
| psychogenic | F44.4 | Conversion disorder with motor symptom or deficit | |
| Roussy-Lévy | G60.0 | Hereditary motor and sensory neuropathy | |
| Sanger-Brown's | G11.2 | Late-onset cerebellar ataxia | |
| spastic hereditary | G11.4 | Hereditary spastic paraplegia | |
| spinocerebellar, X-linked recessive | G11.19 | Other early-onset cerebellar ataxia | |
| telangiectasia | G11.3 | Cerebellar ataxia with defective DNA repair |
Ataxia cerebellar
| with defective DNA repair | G11.3 | Cerebellar ataxia with defective DNA repair | |
| alcoholic | G31.2 | Degeneration of nervous system due to alcohol | |
| early-onset | G11.10 | Early-onset cerebellar ataxia, unspecified | |
| late-onset | G11.2 | Late-onset cerebellar ataxia | |
| with › essential tremor | G11.19 | Other early-onset cerebellar ataxia | |
| with › myoclonus [Hunt's ataxia] | G11.19 | Other early-onset cerebellar ataxia | |
| with › retained tendon reflexes | G11.19 | Other early-onset cerebellar ataxia | |
| in › alcoholism | G31.2 | Degeneration of nervous system due to alcohol | |
| in › myxedema | E03.9 | Hypothyroidism, unspecified | |
| in › neoplastic disease | D49.9 | Neoplasm of unspecified behavior of unspecified site | |
| in › specified disease NEC | G32.81 | Cerebellar ataxia in diseases classified elsewhere |
Ataxia following
| cerebrovascular disease | I69.993 | Ataxia following unspecified cerebrovascular disease | |
| cerebrovascular disease › cerebral infarction | I69.393 | Ataxia following cerebral infarction | |
| cerebrovascular disease › intracerebral hemorrhage | I69.193 | Ataxia following nontraumatic intracerebral hemorrhage | |
| cerebrovascular disease › nontraumatic intracranial hemorrhage NEC | I69.293 | Ataxia following other nontraumatic intracranial hemorrhage | |
| cerebrovascular disease › specified disease NEC | I69.893 | Ataxia following other cerebrovascular disease | |
| cerebrovascular disease › subarachnoid hemorrhage | I69.093 | Ataxia following nontraumatic subarachnoid hemorrhage |
Ataxia gait
| hysterical | F44.4 | Conversion disorder with motor symptom or deficit |
Ataxia gluten
| with celiac disease | K90.0 | Celiac disease |
Ataxia hereditary
Index terms and codes are reproduced from the official ICD-10-CM FY2027 release. The Alphabetic Index is a finding aid — a code must always be verified in the Tabular List before it is reported. Data sources