E25.0 vs Q89.1
E25.0 and Q89.1 can never be reported together. ICD-10-CM declares them mutually exclusive with an Excludes1 note, meaning the two conditions cannot occur in the same patient — so exactly one of them is correct for any given encounter.
Congenital adrenogenital disorders associated with enzyme deficiency
- Chapter 4
- Endocrine, nutritional and metabolic diseases
- Section
- E20-E35
- Congenital adrenal hyperplasia
- 21-Hydroxylase deficiency
- Salt-losing congenital adrenal hyperplasia
- Adrenogenitalism, congenital
- Adrenogenital syndrome › congenital
- Adrenogenital syndrome › salt loss
- Defect, defective › 3-beta-hydroxysteroid dehydrogenase
- Defect, defective › 11-hydroxylase
Congenital malformations of adrenal gland
- Chapter 17
- Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders
- Section
- Q80-Q89
- Aberrant › adrenal gland (congenital)
- Absence › adrenal (of) (organ or part) (complete or partial)
- Accessory › adrenal gland (congenital)
- Agenesis › adrenal
- Anomaly, anomalous › adrenal (congenital) (unspecified type)
These two codes sit in different chapters of the Tabular List, which is usually the clearest signal that they describe different underlying processes rather than different degrees of the same one.
Excludes1 is not always absolute: where two conditions covered by the note are genuinely unrelated, CMS guidance permits reporting both. Document the reasoning rather than assuming it. More on Excludes1 vs Excludes2 · FY2027