FY2027
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Excludes1 pair

D58.1 vs D75.0

D58.1 and D75.0 are not coded together. ICD-10-CM declares them mutually exclusive with an Excludes1 note — the two conditions are not expected to occur together, so exactly one of them is normally correct for a given encounter. The Official Guidelines carve out one exception: if the two conditions are clearly unrelated to each other, both may be reported.

The official note, declared on D75.0
hereditary ovalocytosis (D58.1)
D58.1

Hereditary elliptocytosis

Billable
Chapter 3
Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
Section
D55-D59
Use when the record says
  • Elliptocytosis (congenital)
  • Ovalocytosis (congenital) (hereditary)
Indexed under
  • Dresbach's syndrome (elliptocytosis)
  • Elliptocytosis (congenital) (hereditary)
  • Elliptocytosis › Hb C (disease)
  • Elliptocytosis › hemoglobin disease
  • Syndrome › Dresbach's (elliptocytosis)
D75.0

Familial erythrocytosis

Billable
Chapter 3
Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
Section
D70-D77
Use when the record says
  • Benign polycythemia
  • Familial polycythemia
Indexed under
  • Erythrocytosis › familial
  • Polycythemia › benign (familial)
  • Polycythemia › familial (benign)

Excludes1 is not always absolute: where two conditions covered by the note are genuinely unrelated, CMS guidance permits reporting both. Document the reasoning rather than assuming it. More on Excludes1 vs Excludes2 · FY2027